Emergency Treatment of the HyperKalemic Periodic Paralysis and/or Paramyotonia Congenita Attack First Actions: Hyperkalemic Periodic Paralysis and Paramyotonia Congenita can occur singly or in combination. While most attacks of Hyperkalemic Periodic Paralysis are brief and do not require emergency intervention, occasionally the serum potassium level will be high enough to cause cardiac distress, or muscle stiffness may…
Submitted by deb on Mon, 06/27/2011 – 20:16 Patients with Sodium channel HyperKPP and PMC mutations are at increased risk of Malignant Hyperthermia; It has long been recognized that patients with hyperkalemic periodic paralysis are at increased risk for Malignant Hyperthermia (MH) during surgery, showing as fulminant muscle rigidity as seen in the jaw muscles, rhabdomyolysis, hypercarbia, and…
Submitted by deb on Mon, 06/27/2011 – 02:22 Hao Cheng, MD The use of local anaesthetics on patients with periodic paralysis presents some unusual challenges. Many patients report that these agents trigger weakness or paralysis, a phenomenon which is substantiated in medical literature. Some patients also report that the agents do not produce the desired anaesthesia. The…
Submitted by deb on Mon, 06/27/2011 – 19:16 Periodic Paralysis Patients at Increased Risk of MH Patients with Hyperkalemic periodic paralysis and Paramyotonia Congenita are at increased risk for Malignant Hyperthermia (MH) during surgery. Patients with all types of periodic paralysis often become paralyzed during or after surgery, from stress, chilling in the OR and the use…
Submitted by deb on Tue, 04/12/2016 – 22:54 Adverse reactions to anaesthesia, including life-threatening events, are a serious concern for patients with Periodic Paralysis Disorders. Many of our patients report serious events associated with anesthesia and side effects which may linger for days to months. There is rarely time for a surgical team to comb through journals…
Annabelle SJ Baughan [1] MB FRCP FRCPath,Deborah Cavel-Greant [1],Janice Megalo [1] AAS-MAA, andFrank Weber [2] MD PhD.[1] Periodic Paralysis International (www.hkpp.org)[2] Colonel, Medical Service (Neurology), German Air Force. Military Hospital (Bundeswehrkrankenhaus), 89081 Ulm, & German Air Force Center of Aerospace Medicine, D-82256 Fürstenfelbruck. Medical Adviser, Periodic Paralysis Association;Corresponding author: ASJ Baughan@gmail.com With grateful acknowledgement to…
Annabelle SJ Baughan [1] MB FRCP FRCPath,Deborah Cavel-Greant [1],Janice Megalo [1] AAS-MAA, andFrank Weber [2] MD PhD.[1] Periodic Paralysis International (www.hkpp.org)[2] Colonel, Medical Service (Neurology), German Air Force. Military Hospital (Bundeswehrkrankenhaus), 89081 Ulm, & German Air Force Center of Aerospace Medicine, D-82256 Fürstenfelbruck. Medical Adviser, Periodic Paralysis Association;Corresponding author: ASJ Baughan@gmail.com With grateful acknowledgement to…