Emergency Treatment of the HyperKPP and/or PMC Attack

Submitted by deb on Sat, 08/06/2011 – 22:54 Hyperkalemic Periodic Paralysis and Paramyotonia Congenita can occur singly or in combination.  While most attacks of Hyperkalemic Periodic Paralysis are brief and do not require emergency intervention, occasionally the serum potassium level will be high enough to cause cardiac distress, or muscle stiffness may interfere with respiration.  Attacks of…

Malignant Hyperthermia

Submitted by deb on Mon, 06/27/2011 – 19:16 Periodic Paralysis Patients at Increased Risk of MH Patients with Hyperkalemic periodic paralysis and Paramyotonia Congenita are at increased risk for Malignant Hyperthermia (MH) during surgery.  Patients with all types of periodic paralysis often become paralyzed during or after surgery, from stress, chilling in the OR and the use…

Anaesthesia and peri-operative care in the primary Periodic Paralysis Disorders

Submitted by deb on Tue, 04/12/2016 – 22:54 Adverse reactions to anaesthesia, including life-threatening events, are a serious concern for patients with Periodic Paralysis Disorders. Many of our patients report serious events associated with anesthesia and side effects which may linger for days to months. There is rarely time for a surgical team to comb through journals…

Anesthesia and Peri-Operative Care in the primary Periodic Paralysis Disorders. Part 1: A Review of the Literature

Anesthesia and Peri-Operative Care in the primary Periodic Paralysis Disorders. Part 1: A Review of the Literature

Annabelle SJ Baughan [1] MB FRCP FRCPath,Deborah Cavel-Greant [1],Janice Megalo [1] AAS-MAA, andFrank Weber [2] MD PhD.[1] Periodic Paralysis International (www.hkpp.org)[2] Colonel, Medical Service (Neurology), German Air Force. Military Hospital (Bundeswehrkrankenhaus), 89081 Ulm, & German Air Force Center of Aerospace Medicine, D-82256 Fürstenfelbruck. Medical Adviser, Periodic Paralysis Association;Corresponding author: ASJ Baughan@gmail.com With grateful acknowledgement to…

Anesthesia and Peri-Operative Care  in the primary Periodic Paralysis Disorders. PART 2: Practical Guidelines

Anesthesia and Peri-Operative Care in the primary Periodic Paralysis Disorders. PART 2: Practical Guidelines

Annabelle SJ Baughan [1] MB FRCP FRCPath,Deborah Cavel-Greant [1],Janice Megalo [1] AAS-MAA, andFrank Weber [2] MD PhD.[1] Periodic Paralysis International (www.hkpp.org)[2] Colonel, Medical Service (Neurology), German Air Force. Military Hospital (Bundeswehrkrankenhaus), 89081 Ulm, & German Air Force Center of Aerospace Medicine, D-82256 Fürstenfelbruck. Medical Adviser, Periodic Paralysis Association;Corresponding author: ASJ Baughan@gmail.com With grateful acknowledgement to…